DNA2 Resolves Expanding Flap in Mitochondrial Base Excision Repair

av Copeland, William C., Longley, Matthew J.
Publicerad 2008

Mitochondrial genome maintenance in health and disease

av Copeland, William C., Longley, Matthew J.
Publicerad 2014

DNA Polymerase Gamma in Mitochondrial DNA Replication and Repair

av Copeland, William C., Longley, Matthew J.
I publikationen ScientificWorldJournal (2003)

Analysis of Translesion DNA Synthesis by the Mitochondrial DNA Polymerase γ

av Copeland, William C., Kasiviswanathan, Rajesh, Longley, Matthew J.
I publikationen Methods Mol Biol (2016)

Preparation of Human Mitochondrial Single-Stranded DNA Binding Protein

av Longley, Matthew J., Smith, Leslie A., Copeland, William C.
Publicerad 2009

Polymerase γ efficiently replicates through many natural template barriers but stalls at the HSP1 quadruplex

av Sullivan, Eric D., Longley, Matthew J., Copeland, William C.
I publikationen J Biol Chem (2020)

Modulation of the W748S mutation in DNA polymerase γ by the E1143G polymorphism in mitochondrial disorders

av Chan, Sherine S.L., Longley, Matthew J., Copeland, William C.
Publicerad 2006

Disease Mutations in the Human Mitochondrial DNA Polymerase Thumb Subdomain Impart Severe Defects in Mitochondrial DNA Replication

av Kasiviswanathan, Rajesh, Longley, Matthew J., Chan, Sherine S. L., Copeland, William C.
Publicerad 2009

PURIFICATION AND FUNCTIONAL CHARACTERIZATION OF HUMAN MITOCHONDRIAL DNA POLYMERASE GAMMA HARBORING DISEASE MUTATIONS

av Kasiviswanathan, Rajesh, Longley, Matthew J., Young, Matthew J., Copeland, William C.
Publicerad 2010

Disease Variants of the Human Mitochondrial DNA Helicase Encoded by C10orf2 Differentially Alter Protein Stability, Nucleotide Hydrolysis, and Helicase Activity

av Longley, Matthew J., Humble, Margaret M., Sharief, Farida S., Copeland, William C.
Publicerad 2010

The C-terminal tail of the NEIL1 DNA glycosylase interacts with the human mitochondrial single-stranded DNA binding protein

av Sharma, Nidhi, Chakravarthy, Srinivas, Longley, Matthew J., Copeland, William C., Prakash, Aishwarya
I publikationen DNA Repair (Amst) (2018)

Single-molecule DREEM imaging reveals DNA wrapping around human mitochondrial single-stranded DNA binding protein

av Kaur, Parminder, Longley, Matthew J, Pan, Hai, Wang, Hong, Copeland, William C
I publikationen Nucleic Acids Res (2018)

Long Patch Base Excision Repair in Mammalian Mitochondrial Genomes

av Szczesny, Bartosz, Tann, Anne W., Longley, Matthew J., Copeland, William C., Mitra, Sankar
Publicerad 2008

Synergistic Effects of the in cis T251I and P587L Mitochondrial DNA Polymerase γ Disease Mutations

av DeBalsi, Karen L., Longley, Matthew J., Hoff, Kirsten E., Copeland, William C.
I publikationen J Biol Chem (2017)

Identification of 5′-deoxyribose phosphate lyase activity in human DNA polymerase γ and its role in mitochondrial base excision repair in vitro

av Longley, Matthew J., Prasad, Rajendra, Srivastava, Deepak K., Wilson, Samuel H., Copeland, William C.
Publicerad 1998

Human DNA polymerase θ possesses 5′-dRP lyase activity and functions in single-nucleotide base excision repair in vitro

av Prasad, Rajendra, Longley, Matthew J., Sharief, Farida S., Hou, Esther W., Copeland, William C., Wilson, Samuel H.
Publicerad 2009

Single-molecule level structural dynamics of DNA unwinding by human mitochondrial Twinkle helicase

av Kaur, Parminder, Longley, Matthew J., Pan, Hai, Wang, Wendy, Countryman, Preston, Wang, Hong, Copeland, William C.
I publikationen J Biol Chem (2020)

DNA precursor asymmetries in mammalian tissue mitochondria and possible contribution to mutagenesis through reduced replication fidelity

av Song, Shiwei, Pursell, Zachary F., Copeland, William C., Longley, Matthew J., Kunkel, Thomas A., Mathews, Christopher K.
Publicerad 2005

Biochemical analysis of human POLG2 variants associated with mitochondrial disease

av Young, Matthew J., Longley, Matthew J., Li, Fang-Yuan, Kasiviswanathan, Rajesh, Wong, Lee-Jun, Copeland, William C.
Publicerad 2011

POS5 Gene of Saccharomyces cerevisiae Encodes a Mitochondrial NADH Kinase Required for Stability of Mitochondrial DNA

av Strand, Micheline K., Stuart, Gregory R., Longley, Matthew J., Graziewicz, Maria A., Dominick, Olivia C., Copeland, William C.
Publicerad 2003