The Effects of IRE1, ATF6, and PERK Signaling on adRP-Linked Rhodopsins

Tekijä Chiang, Wei-Chieh Jerry, Lin, Jonathan H.
Julkaisussa Adv Exp Med Biol (2014)

IRE1 directs proteasomal and lysosomal degradation of misfolded rhodopsin

Tekijä Chiang, Wei-Chieh, Messah, Carissa, Lin, Jonathan H.
Julkaistu 2012

Endoplasmic Reticulum-Associated Degradation (ERAD) of Misfolded Glycoproteins and Mutant P23H Rhodopsin in Photoreceptor Cells

Tekijä Kroeger, Heike, Chiang, Wei-Chieh, Lin, Jonathan H.
Julkaistu 2012

Pathomechanisms of ATF6-Associated Cone Photoreceptor Diseases

Tekijä Chiang, Wei-Chieh Jerry, Kroeger, Heike, Chea, Lulu, Lin, Jonathan H.
Julkaisussa Adv Exp Med Biol (2019)

Selective Activation of ATF6 and PERK Endoplasmic Reticulum Stress Signaling Pathways Prevent Mutant Rhodopsin Accumulation

Tekijä Chiang, Wei-Chieh, Hiramatsu, Nobuhiko, Messah, Carissa, Kroeger, Heike, Lin, Jonathan H.
Julkaistu 2012

Endoplasmic Reticulum Stress in Human Photoreceptor Diseases

Tekijä Chan, Priscilla, Stolz, Julia, Kohl, Susanne, Chiang, Wei-Chieh, Lin, Jonathan H.
Julkaisussa Brain Res (2016)

ER stress and unfolded protein response in ocular health and disease

Tekijä Kroeger, Heike, Chiang, Wei-Chieh, Felden, Julia, Nguyen, Amanda, Lin, Jonathan H.
Julkaisussa FEBS J (2018)

Multiple Mechanisms of Unfolded Protein Response–Induced Cell Death

Tekijä Hiramatsu, Nobuhiko, Chiang, Wei-Chieh, Kurt, Timothy D., Sigurdson, Christina J., Lin, Jonathan H.
Julkaisussa Am J Pathol (2015)

Ablation of Chop Transiently Enhances Photoreceptor Survival but Does Not Prevent Retinal Degeneration in Transgenic Mice Expressing Human P23H Rhodopsin

Tekijä Chiang, Wei-Chieh, Joseph, Victory, Yasumura, Douglas, Matthes, Michael T., Lewin, Alfred S., Gorbatyuk, Marina S., Ahern, Kelly, LaVail, Matthew M., Lin, Jonathan H.
Julkaisussa Adv Exp Med Biol (2016)

In Vivo Visualization of Endoplasmic Reticulum Stress in the Retina Using the ERAI Reporter Mouse

Tekijä Alavi, Marcel V., Chiang, Wei-Chieh, Kroeger, Heike, Yasumura, Douglas, Matthes, Michael T., Iwawaki, Takao, LaVail, Matthew M., Gould, Douglas B., Lin, Jonathan H.
Julkaisussa Invest Ophthalmol Vis Sci (2015)

Robust Endoplasmic Reticulum-Associated Degradation of Rhodopsin Precedes Retinal Degeneration

Tekijä Chiang, Wei-Chieh, Kroeger, Heike, Sakami, Sanae, Messah, Carissa, Yasumura, Douglas, Matthes, Michael T., Coppinger, Judith A., Palczewski, Krzysztof, LaVail, Matthew M., Lin, Jonathan H.
Julkaisussa Mol Neurobiol (2014)

Induction of Endoplasmic Reticulum Stress Genes, BiP and Chop, in Genetic and Environmental Models of Retinal Degeneration

Tekijä Kroeger, Heike, Messah, Carissa, Ahern, Kelly, Gee, Jason, Joseph, Victory, Matthes, Michael T., Yasumura, Douglas, Gorbatyuk, Marina S., Chiang, Wei-Chieh, LaVail, Matthew M., Lin, Jonathan H.
Julkaistu 2012

De Novo Prion Aggregates Trigger Autophagy in Skeletal Muscle

Tekijä Joshi-Barr, Shivanjali, Bett, Cyrus, Chiang, Wei-Chieh, Trejo, Margarita, Goebel, Hans H., Sikorska, Beata, Liberski, Pawel, Raeber, Alex, Lin, Jonathan H., Masliah, Eliezer, Sigurdson, Christina J.
Julkaistu 2014

Achromatopsia mutations target sequential steps of ATF6 activation

Tekijä Chiang, Wei-Chieh, Chan, Priscilla, Wissinger, Bernd, Vincent, Ajoy, Skorczyk-Werner, Anna, Krawczyński, Maciej R., Kaufman, Randal J., Tsang, Stephen H., Héon, Elise, Kohl, Susanne, Lin, Jonathan H.
Julkaisussa Proc Natl Acad Sci U S A (2017)

The unfolded protein response regulator ATF6 promotes mesodermal differentiation

Tekijä Kroeger, Heike, Grimsey, Neil, Paxman, Ryan, Chiang, Wei-Chieh, Plate, Lars, Jones, Ying, Shaw, Peter X., Trejo, JoAnn, Tsang, Stephen H., Powers, Evan, Kelly, Jeffery W., Wiseman, R. Luke, Lin, Jonathan H.
Julkaisussa Sci Signal (2018)

Autosomal recessive cone-rod dystrophy can be caused by mutations in the ATF6 gene

Tekijä Skorczyk-Werner, Anna, Chiang, Wei-Chieh, Wawrocka, Anna, Wicher, Katarzyna, Jarmuż-Szymczak, Małgorzata, Kostrzewska-Poczekaj, Magdalena, Jamsheer, Aleksander, Płoski, Rafał, Rydzanicz, Małgorzata, Pojda-Wilczek, Dorota, Weisschuh, Nicole, Wissinger, Bernd, Kohl, Susanne, Lin, Jonathan H, Krawczyński, Maciej R
Julkaisussa Eur J Hum Genet (2017)

Multiexon deletion alleles of ATF6 linked to achromatopsia

Tekijä Lee, Eun-Jin, Chiang, Wei-Chieh Jerry, Kroeger, Heike, Bi, Chloe Xiaoke, Chao, Daniel L., Skowronska-Krawczyk, Dorota, Mastey, Rebecca R., Tsang, Stephen H., Chea, Leon, Kim, Kyle, Lambert, Scott R., Grandjean, Julia M.D., Baumann, Britta, Audo, Isabelle, Kohl, Susanne, Moore, Anthony T., Wiseman, R. Luke, Carroll, Joseph, Lin, Jonathan H.
Julkaisussa JCI Insight (2020)

A 45 nm Stacked CMOS Image Sensor Process Technology for Submicron Pixel †

Tekijä Takahashi, Seiji, Huang, Yi-Min, Sze, Jhy-Jyi, Wu, Tung-Ting, Guo, Fu-Sheng, Hsu, Wei-Cheng, Tseng, Tung-Hsiung, Liao, King, Kuo, Chin-Chia, Chen, Tzu-Hsiang, Chiang, Wei-Chieh, Chuang, Chun-Hao, Chou, Keng-Yu, Chung, Chi-Hsien, Chou, Kuo-Yu, Tseng, Chien-Hsien, Wang, Chuan-Joung, Yaung, Dun-Nien
Julkaisussa Sensors (Basel) (2017)

Mutations in the unfolded protein response regulator ATF6 cause the cone dysfunction disorder achromatopsia

Tekijä Kohl, Susanne, Zobor, Ditta, Chiang, Wei-Chieh, Weisschuh, Nicole, Staller, Jennifer, Menendez, Irene Gonzalez, Chang, Stanley, Beck, Susanne C, Garrido, Marina Garcia, Sothilingam, Vithiyanjali, Seeliger, Mathias W, Stanzial, Franco, Benedicenti, Francesco, Inzana, Francesca, Héon, Elise, Vincent, Ajoy, Beis, Jill, Strom, Tim M, Rudolph, Günther, Roosing, Susanne, den Hollander, Anneke I, Cremers, Frans P M, Lopez, Irma, Ren, Huanan, Moore, Anthony T, Webster, Andrew R, Michaelides, Michel, Koenekoop, Robert K, Zrenner, Eberhart, Kaufman, Randal J, Tsang, Stephen H, Wissinger, Bernd, Lin, Jonathan H
Julkaisussa Nat Genet (2015)