The Effects of IRE1, ATF6, and PERK Signaling on adRP-Linked Rhodopsins

per Chiang, Wei-Chieh Jerry, Lin, Jonathan H.
Publicat a Adv Exp Med Biol (2014)

IRE1 directs proteasomal and lysosomal degradation of misfolded rhodopsin

per Chiang, Wei-Chieh, Messah, Carissa, Lin, Jonathan H.
Publicat 2012

Endoplasmic Reticulum-Associated Degradation (ERAD) of Misfolded Glycoproteins and Mutant P23H Rhodopsin in Photoreceptor Cells

per Kroeger, Heike, Chiang, Wei-Chieh, Lin, Jonathan H.
Publicat 2012

Pathomechanisms of ATF6-Associated Cone Photoreceptor Diseases

per Chiang, Wei-Chieh Jerry, Kroeger, Heike, Chea, Lulu, Lin, Jonathan H.
Publicat a Adv Exp Med Biol (2019)

Selective Activation of ATF6 and PERK Endoplasmic Reticulum Stress Signaling Pathways Prevent Mutant Rhodopsin Accumulation

per Chiang, Wei-Chieh, Hiramatsu, Nobuhiko, Messah, Carissa, Kroeger, Heike, Lin, Jonathan H.
Publicat 2012

Endoplasmic Reticulum Stress in Human Photoreceptor Diseases

per Chan, Priscilla, Stolz, Julia, Kohl, Susanne, Chiang, Wei-Chieh, Lin, Jonathan H.
Publicat a Brain Res (2016)

ER stress and unfolded protein response in ocular health and disease

per Kroeger, Heike, Chiang, Wei-Chieh, Felden, Julia, Nguyen, Amanda, Lin, Jonathan H.
Publicat a FEBS J (2018)

Multiple Mechanisms of Unfolded Protein Response–Induced Cell Death

per Hiramatsu, Nobuhiko, Chiang, Wei-Chieh, Kurt, Timothy D., Sigurdson, Christina J., Lin, Jonathan H.
Publicat a Am J Pathol (2015)

Ablation of Chop Transiently Enhances Photoreceptor Survival but Does Not Prevent Retinal Degeneration in Transgenic Mice Expressing Human P23H Rhodopsin

per Chiang, Wei-Chieh, Joseph, Victory, Yasumura, Douglas, Matthes, Michael T., Lewin, Alfred S., Gorbatyuk, Marina S., Ahern, Kelly, LaVail, Matthew M., Lin, Jonathan H.
Publicat a Adv Exp Med Biol (2016)

In Vivo Visualization of Endoplasmic Reticulum Stress in the Retina Using the ERAI Reporter Mouse

per Alavi, Marcel V., Chiang, Wei-Chieh, Kroeger, Heike, Yasumura, Douglas, Matthes, Michael T., Iwawaki, Takao, LaVail, Matthew M., Gould, Douglas B., Lin, Jonathan H.
Publicat a Invest Ophthalmol Vis Sci (2015)

Robust Endoplasmic Reticulum-Associated Degradation of Rhodopsin Precedes Retinal Degeneration

per Chiang, Wei-Chieh, Kroeger, Heike, Sakami, Sanae, Messah, Carissa, Yasumura, Douglas, Matthes, Michael T., Coppinger, Judith A., Palczewski, Krzysztof, LaVail, Matthew M., Lin, Jonathan H.
Publicat a Mol Neurobiol (2014)

Induction of Endoplasmic Reticulum Stress Genes, BiP and Chop, in Genetic and Environmental Models of Retinal Degeneration

per Kroeger, Heike, Messah, Carissa, Ahern, Kelly, Gee, Jason, Joseph, Victory, Matthes, Michael T., Yasumura, Douglas, Gorbatyuk, Marina S., Chiang, Wei-Chieh, LaVail, Matthew M., Lin, Jonathan H.
Publicat 2012

De Novo Prion Aggregates Trigger Autophagy in Skeletal Muscle

per Joshi-Barr, Shivanjali, Bett, Cyrus, Chiang, Wei-Chieh, Trejo, Margarita, Goebel, Hans H., Sikorska, Beata, Liberski, Pawel, Raeber, Alex, Lin, Jonathan H., Masliah, Eliezer, Sigurdson, Christina J.
Publicat 2014

Achromatopsia mutations target sequential steps of ATF6 activation

per Chiang, Wei-Chieh, Chan, Priscilla, Wissinger, Bernd, Vincent, Ajoy, Skorczyk-Werner, Anna, Krawczyński, Maciej R., Kaufman, Randal J., Tsang, Stephen H., Héon, Elise, Kohl, Susanne, Lin, Jonathan H.
Publicat a Proc Natl Acad Sci U S A (2017)

The unfolded protein response regulator ATF6 promotes mesodermal differentiation

per Kroeger, Heike, Grimsey, Neil, Paxman, Ryan, Chiang, Wei-Chieh, Plate, Lars, Jones, Ying, Shaw, Peter X., Trejo, JoAnn, Tsang, Stephen H., Powers, Evan, Kelly, Jeffery W., Wiseman, R. Luke, Lin, Jonathan H.
Publicat a Sci Signal (2018)

Autosomal recessive cone-rod dystrophy can be caused by mutations in the ATF6 gene

per Skorczyk-Werner, Anna, Chiang, Wei-Chieh, Wawrocka, Anna, Wicher, Katarzyna, Jarmuż-Szymczak, Małgorzata, Kostrzewska-Poczekaj, Magdalena, Jamsheer, Aleksander, Płoski, Rafał, Rydzanicz, Małgorzata, Pojda-Wilczek, Dorota, Weisschuh, Nicole, Wissinger, Bernd, Kohl, Susanne, Lin, Jonathan H, Krawczyński, Maciej R
Publicat a Eur J Hum Genet (2017)

Multiexon deletion alleles of ATF6 linked to achromatopsia

per Lee, Eun-Jin, Chiang, Wei-Chieh Jerry, Kroeger, Heike, Bi, Chloe Xiaoke, Chao, Daniel L., Skowronska-Krawczyk, Dorota, Mastey, Rebecca R., Tsang, Stephen H., Chea, Leon, Kim, Kyle, Lambert, Scott R., Grandjean, Julia M.D., Baumann, Britta, Audo, Isabelle, Kohl, Susanne, Moore, Anthony T., Wiseman, R. Luke, Carroll, Joseph, Lin, Jonathan H.
Publicat a JCI Insight (2020)

A 45 nm Stacked CMOS Image Sensor Process Technology for Submicron Pixel †

per Takahashi, Seiji, Huang, Yi-Min, Sze, Jhy-Jyi, Wu, Tung-Ting, Guo, Fu-Sheng, Hsu, Wei-Cheng, Tseng, Tung-Hsiung, Liao, King, Kuo, Chin-Chia, Chen, Tzu-Hsiang, Chiang, Wei-Chieh, Chuang, Chun-Hao, Chou, Keng-Yu, Chung, Chi-Hsien, Chou, Kuo-Yu, Tseng, Chien-Hsien, Wang, Chuan-Joung, Yaung, Dun-Nien
Publicat a Sensors (Basel) (2017)

Mutations in the unfolded protein response regulator ATF6 cause the cone dysfunction disorder achromatopsia

per Kohl, Susanne, Zobor, Ditta, Chiang, Wei-Chieh, Weisschuh, Nicole, Staller, Jennifer, Menendez, Irene Gonzalez, Chang, Stanley, Beck, Susanne C, Garrido, Marina Garcia, Sothilingam, Vithiyanjali, Seeliger, Mathias W, Stanzial, Franco, Benedicenti, Francesco, Inzana, Francesca, Héon, Elise, Vincent, Ajoy, Beis, Jill, Strom, Tim M, Rudolph, Günther, Roosing, Susanne, den Hollander, Anneke I, Cremers, Frans P M, Lopez, Irma, Ren, Huanan, Moore, Anthony T, Webster, Andrew R, Michaelides, Michel, Koenekoop, Robert K, Zrenner, Eberhart, Kaufman, Randal J, Tsang, Stephen H, Wissinger, Bernd, Lin, Jonathan H
Publicat a Nat Genet (2015)