Location- and sex-specific differences in weight and motor coordination in two commonly used mouse strains

Por Kovács, Attila D., Pearce, David A.
Publicado em 2013

Finding the most appropriate mouse model of juvenile CLN3 (Batten) disease for therapeutic studies: the importance of genetic background and gender

Por Kovács, Attila D., Pearce, David A.
Publicado no Dis Model Mech (2015)

Attenuation of AMPA receptor activity improves motor skills in a mouse model of juvenile Batten disease

Por Kovács, Attila D., Pearce, David A.
Publicado no Exp Neurol (2007)

Altered sensitivity to excitotoxic cell death and glutamate receptor expression between two commonly studied mouse strains

Por Finn, Rozzy, Kovács, Attila D., Pearce, David A.
Publicado em 2010

Altered sensitivity of cerebellar granule cells to glutamate receptor overactivation in the Cln3(Δex7/8)-knock-in mouse model of juvenile neuronal ceroid lipofuscinosis

Por Finn, Rozzy, Kovács, Attila D., Pearce, David A.
Publicado em 2011

Altered glutamate receptor function in the cerebellum of the Ppt1(−/−) mouse, a murine model of infantile neuronal ceroid lipofuscinosis

Por Finn, Rozzy, Kovács, Attila D., Pearce, David A.
Publicado em 2011

Treatment of the Ppt1(−/−) Mouse Model of Infantile Neuronal Ceroid Lipofuscinosis with the NMDA Receptor Antagonist Memantine

Por Finn, Rozzy, Kovács, Attila D., Pearce, David A.
Publicado em 2013

The Human Synaptic Vesicle Protein, SV2A, Functions as a Galactose Transporter in Saccharomyces cerevisiae

Por Madeo, Marianna, Kovács, Attila D., Pearce, David A.
Publicado no J Biol Chem (2014)

Abnormally increased surface expression of AMPA receptors in the cerebellum, cortex and striatum of Cln3(−/−) mice

Por Kovács, Attila D., Hof, Caitlin, Pearce, David A.
Publicado no Neurosci Lett (2015)

Decreased sensitivity of palmitoyl protein thioesterase 1-deficient neurons to chemical anoxia

Por Meyer, Meredith, Kovács, Attila D., Pearce, David A.
Publicado no Metab Brain Dis (2016)

Seizure Susceptibility, Phenotype, and Resultant Growth Delay in the nclf and mnd Mouse Models of Neuronal Ceroid Lipofuscinoses

Por Kriscenski-Perry, Elizabeth, Kovács, Attila D., Pearce, David A.
Publicado em 2013

The novel Cln1(R151X) mouse model of infantile neuronal ceroid lipofuscinosis (INCL) for testing nonsense suppression therapy

Por Miller, Jake N., Kovács, Attila D., Pearce, David A.
Publicado no Hum Mol Genet (2015)

Antigen presenting cell abnormalities in the Cln3(−/−) mouse model of juvenile neuronal ceroid lipofuscinosis

Por Hersrud, Samantha L., Kovács, Attila D., Pearce, David A.
Publicado no Biochim Biophys Acta (2016)

Tissue‐specific variation in nonsense mutant transcript level and drug‐induced read‐through efficiency in the Cln1 (R151X) mouse model of INCL

Por Thada, Vaughn, Miller, Jake N., Kovács, Attila D., Pearce, David A.
Publicado no J Cell Mol Med (2015)

Age-dependent therapeutic effect of memantine in a mouse model of juvenile Batten disease

Por Kovács, Attila D., Saje, Angelika, Wong, Andrew, Ramji, Serena, Cooper, Jonathan D., Pearce, David A.
Publicado em 2012

Osmotic Stress Changes the Expression and Subcellular Localization of the Batten Disease Protein CLN3

Por Getty, Amanda, Kovács, Attila D., Lengyel-Nelson, Tímea, Cardillo, Andrew, Hof, Caitlin, Chan, Chun-Hung, Pearce, David A.
Publicado em 2013

Temporary inhibition of AMPA receptors induces a prolonged improvement of motor performance in a mouse model of juvenile Batten disease

Por Kovács, Attila D., Saje, Angelika, Wong, Andrew, Szénási, Gábor, Kiricsi, Péter, Szabó, Éva, Cooper, Jonathan D., Pearce, David A.
Publicado em 2010

A novel porcine model of ataxia telangiectasia reproduces neurological features and motor deficits of human disease

Por Beraldi, Rosanna, Chan, Chun-Hung, Rogers, Christopher S., Kovács, Attila D., Meyerholz, David K., Trantzas, Constantin, Lambertz, Allyn M., Darbro, Benjamin W., Weber, Krystal L., White, Katherine A.M., Rheeden, Richard V., Kruer, Michael C., Dacken, Brian A., Wang, Xiao-Jun, Davis, Bryan T., Rohret, Judy A., Struzynski, Jason T., Rohret, Frank A., Weimer, Jill M., Pearce, David A.
Publicado no Hum Mol Genet (2015)