Progress toward Fulfilling the Potential of Immunomodulation in Childhood Neurodegeneration?

od Cooper, Jonathan D., Nelvagal, Hemanth R.
izdano v Mol Ther (2017)

Pathogenesis and Therapies for Infantile Neuronal Ceroid Lipofuscinosis (infantile CLN1 disease)

od Hawkins-Salsbury, Jacqueline A., Cooper, Jonathan D., Sands, Mark S.
izdano v Biochim Biophys Acta (2013)

Selectivity and Types of Cell Death in the Neuronal Ceroid Lipofuscinoses (NCLs)

od Mitchison, Hannah M., Lim, Ming J., Cooper, Jonathan D.
izdano v Brain Pathol (2006)

Anti-Inflammatory Impact of Minocycline in a Mouse Model of Tauopathy

od Garwood, Claire J., Cooper, Jonathan D., Hanger, Diane P., Noble, Wendy
Izdano 2010

Activation of Non‐neuronal Cells within the Prenatal Developing Brain of Sheep with Neuronal Ceroid Lipofuscinosis

od Kay, Graham W., Palmer, David N., Rezaie, Payam, Cooper, Jonathan D.
izdano v Brain Pathol (2006)

Hippocampal Pathology in the Human Neuronal Ceroid‐Lipofuscinoses: Distinct Patterns of Storage Deposition, Neurodegeneration and Glial Activation

od Tyynelä, Jaana, Cooper, Jonathan D, Khan, M Nadeem, Shemilt, Stephen JA, Haltia, Matti
izdano v Brain Pathol (2006)

Apparent Loss and Hypertrophy of Interneurons in a Mouse Model of Neuronal Ceroid Lipofuscinosis: Evidence for Partial Response to Insulin-Like Growth Factor-1 Treatment

od Cooper, Jonathan D., Messer, Anne, Feng, Andrew K., Chua-Couzens, Jane, Mobley, William C.
izdano v J Neurosci (1999)

Location and connectivity determine GABAergic interneuron survival in the brains of South Hampshire sheep with CLN6 neuronal ceroid lipofuscinosis

od Oswald, Manfred J, Palmer, David N, Kay, Graham W, Barwell, Karen J, Cooper, Jonathan D
Izdano 2008

Cerebellar Pathology and Motor Deficits in the Palmitoyl Protein Thioesterase 1-Deficient Mouse

od Macauley, Shannon L., Wozniak, David F., Kielar, Catherine, Tan, Yun, Cooper, Jonathan D., Sands, Mark S.
Izdano 2009

Age-dependent therapeutic effect of memantine in a mouse model of juvenile Batten disease

od Kovács, Attila D., Saje, Angelika, Wong, Andrew, Ramji, Serena, Cooper, Jonathan D., Pearce, David A.
Izdano 2012

Neurodegeneration and Epilepsy in a Zebrafish Model of CLN3 Disease (Batten Disease)

od Wager, Kim, Zdebik, Anselm A., Fu, Sonia, Cooper, Jonathan D., Harvey, Robert J., Russell, Claire
izdano v PLoS One (2016)

Enhanced expression of manganese-dependent superoxide dismutase in human and sheep CLN6 tissues.

od Heine, Claudia, Tyynelä, Jaana, Cooper, Jonathan D, Palmer, David N, Elleder, Milan, Kohlschütter, Alfried, Braulke, Thomas
Izdano 2003

Early glial activation, synaptic changes and axonal pathology in the thalamocortical system of Niemann–Pick type C1 mice

od Pressey, Sarah N.R., Smith, David A., Wong, Andrew M.S., Platt, Frances M., Cooper, Jonathan D.
Izdano 2012

A Murine Model of Variant Late Infantile Ceroid Lipofuscinosis Recapitulates Behavioral and Pathological Phenotypes of Human Disease

od Morgan, Jeremy P., Magee, Helen, Wong, Andrew, Nelson, Tarah, Koch, Bettina, Cooper, Jonathan D., Weimer, Jill M.
Izdano 2013

Combination small molecule PPT1 mimetic and CNS-directed gene therapy as a treatment for infantile neuronal ceroid lipofuscinosis

od Roberts, Marie S., Macauley, Shannon L., Wong, Andrew M., Yilmas, Denis, Hohm, Sarah, Cooper, Jonathan D., Sands, Mark S.
Izdano 2012

Synergistic effects of treating the spinal cord and brain in CLN1 disease

od Shyng, Charles, Nelvagal, Hemanth R., Dearborn, Joshua T., Tyynelä, Jaana, Schmidt, Robert E., Sands, Mark S., Cooper, Jonathan D.
izdano v Proc Natl Acad Sci U S A (2017)

Brain gene expression profiles of Cln1 and Cln5 deficient mice unravels common molecular pathways underlying neuronal degeneration in NCL diseases

od von Schantz, Carina, Saharinen, Juha, Kopra, Outi, Cooper, Jonathan D, Gentile, Massimiliano, Hovatta, Iiris, Peltonen, Leena, Jalanko, Anu
Izdano 2008

Synergistic effects of CNS-directed gene therapy and bone marrow transplantation in the murine model of infantile neuronal ceroid lipofuscinosis

od Macauley, Shannon L., Roberts, Marie S., Wong, Andrew M., McSloy, Francesca, Reddy, Adarsh S., Cooper, Jonathan D., Sands, Mark S.
Izdano 2012

Correction: Disruption of the Autophagy-Lysosome Pathway Is Involved in Neuropathology of the nclf Mouse Model of Neuronal Ceroid Lipofuscinosis

od Thelen, Melanie, Damme, Markus, Schweizer, Michaela, Hagel, Christian, Wong, Andrew M.S., Cooper, Jonathan D., Braulke, Thomas, Galliciotti, Giovanna
Izdano 2012

Evolution of structural abnormalities in the rat brain following in utero exposure to maternal immune activation: A longitudinal in vivo MRI study

od Crum, William R., Sawiak, Stephen J., Chege, Winfred, Cooper, Jonathan D., Williams, Steven C.R., Vernon, Anthony C.
izdano v Brain Behav Immun (2017)