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Remodeling the endoplasmic reticulum proteostasis network restores proteostasis of pathogenic GABA(A) receptors

Biogenesis of membrane proteins is controlled by the protein homeostasis (proteostasis) network. We have been focusing on protein quality control of γ-aminobutyric acid type A (GABA(A)) receptors, the major inhibitory neurotransmitter-gated ion channels in mammalian central nervous system. Proteosta...

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Dades bibliogràfiques
Publicat a:PLoS One
Autors principals: Fu, Yan-Lin, Han, Dong-Yun, Wang, Ya-Juan, Di, Xiao-Jing, Yu, Hai-Bo, Mu, Ting-Wei
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6258528/
https://ncbi.nlm.nih.gov/pubmed/30481215
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0207948
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