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Using pharmacological chaperones to restore proteostasis

Normal organismal physiology depends on the maintenance of proteostasis in each cellular compartment to achieve a delicate balance between protein synthesis, folding, trafficking, and degradation while minimizing misfolding and aggregation. Defective proteostasis leads to numerous protein misfolding...

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Detalhes bibliográficos
Main Authors: Wang, Ya-Juan, Di, Xiao-Jing, Mu, Ting-Wei
Formato: Artigo
Idioma:Inglês
Publicado em: 2014
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4070435/
https://ncbi.nlm.nih.gov/pubmed/24747662
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.phrs.2014.04.002
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