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ADAMTS13 Autoantibodies Cloned from Patients with Acquired Thrombotic Thrombocytopenic Purpura: 1. Structural and functional characterization in vitro

BACKGROUND: Acquired thrombotic thrombocytopenia purpura (TTP) is a life-threatening illness caused by autoantibodies that decrease the activity of ADAMTS13, the von Willebrand Factor cleaving protease. Despite efficacy of plasma exchange, mortality remains high and relapse is common. Improved thera...

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Publicat a:Transfusion
Autors principals: Ostertag, Eric M., Kacir, Stephen, Thiboutot, Michelle, Gulendran, Gayathri, Zheng, X. Long, Cines, Douglas B., Siegel, Don L.
Format: Artigo
Idioma:Inglês
Publicat: 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4938786/
https://ncbi.nlm.nih.gov/pubmed/27040144
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/trf.13584
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