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Nucleocytoplasmic transport in C9orf72-mediated ALS/FTD

A GGGGCC hexanucleotide repeat expansion in C9orf72 is the most common genetic cause of familial amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD). Recent studies indicate that disruption of nucleocytoplasmic transport pathways play a critical role in the pathogenesis of C9orf72-...

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Dades bibliogràfiques
Publicat a:Nucleus
Autors principals: Zhang, Ke, Grima, Jonathan C., Rothstein, Jeffery D., Lloyd, Thomas E.
Format: Artigo
Idioma:Inglês
Publicat: Taylor & Francis 2016
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4916865/
https://ncbi.nlm.nih.gov/pubmed/27116041
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1080/19491034.2016.1172152
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