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A multifunctional, multi-pathway intracellular localization signal in Huntingtin

Nuclear accumulation of the polyglutamine-expanded mutant huntingtin protein remains one of the most predictive cell biological phenotypes of Huntington’s disease (HD) progression in patient brain samples and mouse models of the disease. Yet, the relationship between huntingtin nuclear import, neuro...

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Autores principales: Desmond, Carly R., Maiuri, Tamara, Truant, Ray
Formato: Artigo
Lenguaje:Inglês
Publicado: Landes Bioscience 2013
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3609847/
https://ncbi.nlm.nih.gov/pubmed/23750301
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4161/cib.23318
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