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Kinetically competing huntingtin aggregation pathways control amyloid polymorphism and properties

In polyglutamine (polyQ) containing fragments of the Huntington’s disease protein huntingtin (htt), the N-terminal 17 amino acid htt(NT) segment serves as the core of α-helical oligomers whose reversible assembly locally concentrates the polyQ segments, thereby facilitating polyQ amyloid nucleation....

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Dettagli Bibliografici
Autori principali: Jayaraman, Murali, Mishra, Rakesh, Kodali, Ravindra, Thakur, Ashwani K., Koharudin, Leonardus M. I., Gronenborn, Angela M., Wetzel, Ronald
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3394396/
https://ncbi.nlm.nih.gov/pubmed/22432740
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1021/bi3000929
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