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Endoplasmic Reticulum Ca(2+) Increases Enhance Mutant Glucocerebrosidase Proteostasis

Altering intracellular calcium levels is known to partially restore mutant enzyme homeostasis in several lysosomal storage diseases, but why? We hypothesize that endoplasmic reticulum (ER) calcium level increases enhance the folding, trafficking and function of these mutant misfolding/degradation-pr...

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Bibliografski detalji
Glavni autori: Ong, Derrick Sek Tong, Mu, Ting-Wei, Palmer, Amy E., Kelly, Jeffery W.
Format: Artigo
Jezik:Inglês
Izdano: 2010
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC2873071/
https://ncbi.nlm.nih.gov/pubmed/20453863
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/nchembio.368
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