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Endoplasmic Reticulum Ca(2+) Increases Enhance Mutant Glucocerebrosidase Proteostasis

Altering intracellular calcium levels is known to partially restore mutant enzyme homeostasis in several lysosomal storage diseases, but why? We hypothesize that endoplasmic reticulum (ER) calcium level increases enhance the folding, trafficking and function of these mutant misfolding/degradation-pr...

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Autors principals: Ong, Derrick Sek Tong, Mu, Ting-Wei, Palmer, Amy E., Kelly, Jeffery W.
Format: Artigo
Idioma:Inglês
Publicat: 2010
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2873071/
https://ncbi.nlm.nih.gov/pubmed/20453863
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/nchembio.368
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