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Replisome stalling and stabilization at CGG repeats that are responsible for chromosomal fragility

Expanded CGG repeats cause chromosomal fragility and hereditary neurological disorders in humans. Replication forks stall at CGG repeats in a length-dependent manner in primate cells and in yeast. Yeast Tof1 and Mrc1 proteins facilitate replication fork progression through CGG repeats. Remarkably, t...

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Autori principali: Voineagu, Irina, Surka, Christine F., Shishkin, Alexander A., Krasilnikova, Maria M., Mirkin, Sergei M.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2009
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2837601/
https://ncbi.nlm.nih.gov/pubmed/19136957
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/nsmb.1527
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