Mapping of a Myosin-binding Domain and a Regulatory Phosphorylation Site in M-Protein, a Structural Protein of the Sarcomeric M Band

Por Obermann, Wolfgang M.J., van der Ven, Peter F.M., Steiner, Frank, Weber, Klaus, Fürst, Dieter O.
Publicado em 1998

Filamin C-related myopathies: pathology and mechanisms

Por Fürst, Dieter O., Goldfarb, Lev G., Kley, Rudolf A., Vorgerd, Matthias, Olivé, Montse, van der Ven, Peter F. M.
Publicado no Acta Neuropathol (2012)

Impairment of protein degradation in myofibrillar myopathy caused by FLNC/filamin C mutations

Por Kley, Rudolf A., van der Ven, Peter F.M., Olivé, Montse, Höhfeld, Jörg, Goldfarb, Lev G., Fürst, Dieter O., Vorgerd, Matthias
Publicado em 2013

Breaking sarcomeres by in vitro exercise

Por Orfanos, Zacharias, Gödderz, Markus P. O., Soroka, Ekaterina, Gödderz, Tobias, Rumyantseva, Anastasia, van der Ven, Peter F. M., Hawke, Thomas J., Fürst, Dieter O.
Publicado no Sci Rep (2016)

Translocation of molecular chaperones to the titin springs is common in skeletal myopathy patients and affects sarcomere function

Por Unger, Andreas, Beckendorf, Lisa, Böhme, Pierre, Kley, Rudolf, von Frieling-Salewsky, Marion, Lochmüller, Hanns, Schröder, Rolf, Fürst, Dieter O., Vorgerd, Matthias, Linke, Wolfgang A.
Publicado no Acta Neuropathol Commun (2017)

The novel cardiac z-disc protein CEFIP regulates cardiomyocyte hypertrophy by modulating calcineurin signaling

Por Dierck, Franziska, Kuhn, Christian, Rohr, Claudia, Hille, Susanne, Braune, Julia, Sossalla, Samuel, Molt, Sibylle, van der Ven, Peter F. M., Fürst, Dieter O., Frey, Norbert
Publicado no J Biol Chem (2017)

A Mutation in the Dimerization Domain of Filamin C Causes a Novel Type of Autosomal Dominant Myofibrillar Myopathy

Por Vorgerd, Matthias, van der Ven, Peter F. M., Bruchertseifer, Vera, Löwe, Thomas, Kley, Rudolf A., Schröder, Rolf, Lochmüller, Hanns, Himmel, Mirko, Koehler, Katrin, Fürst, Dieter O., Huebner, Angela
Publicado em 2005

Indications for a Novel Muscular Dystrophy Pathway: γ-Filamin, the Muscle-Specific Filamin Isoform, Interacts with Myotilin

Por van der Ven, Peter F.M., Wiesner, Sebastian, Salmikangas, Paula, Auerbach, Daniel, Himmel, Mirko, Kempa, Stefan, Hayeß, Katrin, Pacholsky, Dirk, Taivainen, Anu, Schröder, Rolf, Carpén, Olli, Fürst, Dieter O.
Publicado em 2000

Interplay of Matrix Stiffness and c-SRC in Hepatic Fibrosis

Por Görtzen, Jan, Schierwagen, Robert, Bierwolf, Jeanette, Klein, Sabine, Uschner, Frank E., van der Ven, Peter F., Fürst, Dieter O., Strassburg, Christian P., Laleman, Wim, Pollok, Jörg-Matthias, Trebicka, Jonel
Publicado no Front Physiol (2015)

Xirp Proteins Mark Injured Skeletal Muscle in Zebrafish

Por Otten, Cécile, van der Ven, Peter F., Lewrenz, Ilka, Paul, Sandeep, Steinhagen, Almut, Busch-Nentwich, Elisabeth, Eichhorst, Jenny, Wiesner, Burkhard, Stemple, Derek, Strähle, Uwe, Fürst, Dieter O., Abdelilah-Seyfried, Salim
Publicado em 2012

Identification of Xin-repeat proteins as novel ligands of the SH3 domains of nebulin and nebulette and analysis of their interaction during myofibril formation and remodeling

Por Eulitz, Stefan, Sauer, Florian, Pelissier, Marie-Cecile, Boisguerin, Prisca, Molt, Sibylle, Schuld, Julia, Orfanos, Zacharias, Kley, Rudolf A., Volkmer, Rudolf, Wilmanns, Matthias, Kirfel, Gregor, van der Ven, Peter F. M., Fürst, Dieter O.
Publicado em 2013

Myofibrillar Z-discs Are a Protein Phosphorylation Hot Spot with Protein Kinase C (PKCα) Modulating Protein Dynamics

Por Reimann, Lena, Wiese, Heike, Leber, Yvonne, Schwäble, Anja N., Fricke, Anna L., Rohland, Anne, Knapp, Bettina, Peikert, Christian D., Drepper, Friedel, van der Ven, Peter F. M., Radziwill, Gerald, Fürst, Dieter O., Warscheid, Bettina
Publicado no Mol Cell Proteomics (2017)

Statins activate the canonical hedgehog-signaling and aggravate non-cirrhotic portal hypertension, but inhibit the non-canonical hedgehog signaling and cirrhotic portal hypertensio...

Por Uschner, Frank E., Ranabhat, Ganesh, Choi, Steve S., Granzow, Michaela, Klein, Sabine, Schierwagen, Robert, Raskopf, Esther, Gautsch, Sebastian, van der Ven, Peter F. M., Fürst, Dieter O., Strassburg, Christian P., Sauerbruch, Tilman, Mae Diehl, Anna, Trebicka, Jonel
Publicado no Sci Rep (2015)

A Combined Laser Microdissection and Mass Spectrometry Approach Reveals New Disease Relevant Proteins Accumulating in Aggregates of Filaminopathy Patients

Por Kley, Rudolf A., Maerkens, Alexandra, Leber, Yvonne, Theis, Verena, Schreiner, Anja, van der Ven, Peter F. M., Uszkoreit, Julian, Stephan, Christian, Eulitz, Stefan, Euler, Nicole, Kirschner, Janbernd, Müller, Klaus, Meyer, Helmut E., Tegenthoff, Martin, Fürst, Dieter O., Vorgerd, Matthias, Müller, Thorsten, Marcus, Katrin
Publicado em 2013

Pathophysiology of protein aggregation and extended phenotyping in filaminopathy

Por Kley, Rudolf A., Serdaroglu-Oflazer, Piraye, Leber, Yvonne, Odgerel, Zagaa, van der Ven, Peter F. M., Olivé, Montse, Ferrer, Isidro, Onipe, Adekunle, Mihaylov, Mariya, Bilbao, Juan M., Lee, Hee S., Höhfeld, Jörg, Djinović-Carugo, Kristina, Kong, Kester, Tegenthoff, Martin, Peters, Sören A., Stenzel, Werner, Vorgerd, Matthias, Goldfarb, Lev G., Fürst, Dieter O.
Publicado em 2012

Angiotensin-II Type 1 Receptor-Mediated Janus Kinase 2 Activation Induces Liver Fibrosis

Por Granzow, Michaela, Schierwagen, Robert, Klein, Sabine, Kowallick, Benita, Huss, Sebastian, Linhart, Markus, Reza Mazar, Irela G., Görtzen, Jan, Vogt, Annabelle, Schildberg, Frank A., Gonzalez-Carmona, Maria A., Wojtalla, Alexandra, Krämer, Benjamin, Nattermann, Jacob, Siegmund, Sören V., Werner, Nikos, Fürst, Dieter O., Laleman, Wim, Knolle, Percy, Shah, Vijay H., Sauerbruch, Tilman, Trebicka, Jonel
Publicado no Hepatology (2014)

Mutations in the N-terminal Actin-Binding Domain of Filamin C Cause a Distal Myopathy

Por Duff, Rachael M., Tay, Valerie, Hackman, Peter, Ravenscroft, Gianina, McLean, Catriona, Kennedy, Paul, Steinbach, Alina, Schöffler, Wiebke, van der Ven, Peter F.M., Fürst, Dieter O., Song, Jaeguen, Djinović-Carugo, Kristina, Penttilä, Sini, Raheem, Olayinka, Reardon, Katrina, Malandrini, Alessandro, Gambelli, Simona, Villanova, Marcello, Nowak, Kristen J., Williams, David R., Landers, John E., Brown, Robert H., Udd, Bjarne, Laing, Nigel G.
Publicado em 2011