Measurement of Mitochondrial dNTP Pools

Autor Martí, Ramon, Dorado, Beatriz, Hirano, Michio
Vydáno v Methods Mol Biol (2012)

Molecular and Cellular Mechanisms Driving Cardiovascular Disease in Hutchinson-Gilford Progeria Syndrome: Lessons Learned from Animal Models

Autor Benedicto, Ignacio, Dorado, Beatriz, Andrés, Vicente
Vydáno v Cells (2021)

Onset and organ specificity of Tk2 deficiency depends on Tk1 down-regulation and transcriptional compensation

Autor Dorado, Beatriz, Area, Estela, Akman, Hasan O., Hirano, Michio
Vydáno 2011

Tissue-specific oxidative stress and loss of mitochondria in CoQ-deficient Pdss2 mutant mice

Autor Quinzii, Catarina M., Garone, Caterina, Emmanuele, Valentina, Tadesse, Saba, Krishna, Sindu, Dorado, Beatriz, Hirano, Michio
Vydáno 2013

Vascular Smooth Muscle Cell-Specific Progerin Expression Provokes Contractile Impairment in a Mouse Model of Hutchinson-Gilford Progeria Syndrome that Is Ameliorated by Nitrite Tre...

Autor del Campo, Lara, Sánchez-López, Amanda, González-Gómez, Cristina, Andrés-Manzano, María Jesús, Dorado, Beatriz, Andrés, Vicente
Vydáno v Cells (2020)

Thymidine Kinase 2 Deficiency-Induced Mitochondrial DNA Depletion Causes Abnormal Development of Adipose Tissues and Adipokine Levels in Mice

Autor Villarroya, Joan, Dorado, Beatriz, Vilà, Maya R., Garcia-Arumí, Elena, Domingo, Pere, Giralt, Marta, Hirano, Michio, Villarroya, Francesc
Vydáno 2011

Targeted impairment of thymidine kinase 2 expression in cells induces mitochondrial DNA depletion and reveals molecular mechanisms of compensation of mitochondrial respiratory acti...

Autor Villarroya, Joan, Lara, Mari-Carmen, Dorado, Beatriz, Garrido, Marta, García-Arumí, Elena, Meseguer, Anna, Hirano, Michio, Vilà, Maya R.
Vydáno v Biochem Biophys Res Commun (2011)

Metabolic Activity Determines Efficacy of Macroautophagic Clearance of Pathological Oligomeric α-Synuclein

Autor Yu, Wai Haung, Dorado, Beatriz, Figueroa, Helen Yvette, Wang, Lili, Planel, Emmanuel, Cookson, Mark R., Clark, Lorraine N., Duff, Karen E.
Vydáno 2009

Thymidine kinase 2 (H126N) knockin mice show the essential role of balanced deoxynucleotide pools for mitochondrial DNA maintenance

Autor Akman, Hasan O., Dorado, Beatriz, López, Luis C., García-Cazorla, Ángeles, Vilà, Maya R., Tanabe, Lauren M., Dauer, William T., Bonilla, Eduardo, Tanji, Kurenai, Hirano, Michio
Vydáno 2008

Unbalanced deoxynucleotide pools cause mitochondrial DNA instability in thymidine phosphorylase-deficient mice

Autor López, Luis C., Akman, Hasan O., García-Cazorla, Ángeles, Dorado, Beatriz, Martí, Ramón, Nishino, Ichizo, Tadesse, Saba, Pizzorno, Giuseppe, Shungu, Dikoma, Bonilla, Eduardo, Tanji, Kurenai, Hirano, Michio
Vydáno 2009

Decreased hippocampal expression of Calbindin D(28K) and cognitive impairment in MELAS

Autor Emmanuele, Valentina, Garcia-Cazorla, Angels, Huang, Hua-Bin, Çoku, Jorida, Dorado, Beatriz, Cortes, Etty P, Engelstad, Kristin, De Vivo, Darryl C., DiMauro, Salvatore, Bonilla, Eduardo, Tanji, Kurenai
Vydáno 2012

Lamin A/C augments Th1 differentiation and response against vaccinia virus and Leishmania major

Autor Toribio-Fernández, Raquel, Zorita, Virginia, Rocha-Perugini, Vera, Iborra, Salvador, Martínez del Hoyo, Gloria, Chevre, Raphael, Dorado, Beatriz, Sancho, David, Sanchez-Madrid, Francisco, Andrés, Vicente, Gonzalez-Granado, Jose-Maria
Vydáno v Cell Death Dis (2018)

Identification of common cardiometabolic alterations and deregulated pathways in mouse and pig models of aging

Autor Fanjul, Víctor, Jorge, Inmaculada, Camafeita, Emilio, Macías, Álvaro, González‐Gómez, Cristina, Barettino, Ana, Dorado, Beatriz, Andrés‐Manzano, María Jesús, Rivera‐Torres, José, Vázquez, Jesús, López‐Otín, Carlos, Andrés, Vicente
Vydáno v Aging Cell (2020)

Association of Glucocerebrosidase Mutations With Dementia With Lewy Bodies

Autor Clark, Lorraine N., Kartsaklis, Lykourgos A., Wolf Gilbert, Rebecca, Dorado, Beatriz, Ross, Barbara M., Kisselev, Sergey, Verbitsky, Miguel, Mejia-Santana, Helen, Cote, Lucien J., Andrews, Howard, Vonsattel, Jean-Paul, Fahn, Stanley, Mayeux, Richard, Honig, Lawrence S., Marder, Karen
Vydáno 2009

Reactive oxygen species, oxidative stress, and cell death correlate with level of CoQ(10) deficiency

Autor Quinzii, Catarina M., López, Luis C., Gilkerson, Robert W., Dorado, Beatriz, Coku, Jorida, Naini, Ali B., Lagier-Tourenne, Clotilde, Schuelke, Markus, Salviati, Leonardo, Carrozzo, Rosalba, Santorelli, Filippo, Rahman, Shamima, Tazir, Meriem, Koenig, Michel, DiMauro, Salvatore, Hirano, Michio
Vydáno 2010

Generation and characterization of a novel knockin minipig model of Hutchinson-Gilford progeria syndrome

Autor Dorado, Beatriz, Pløen, Gro Grunnet, Barettino, Ana, Macías, Alvaro, Gonzalo, Pilar, Andrés-Manzano, María Jesús, González-Gómez, Cristina, Galán-Arriola, Carlos, Alfonso, José Manuel, Lobo, Manuel, López-Martín, Gonzalo J., Molina, Antonio, Sánchez-Sánchez, Raúl, Gadea, Joaquín, Sánchez-González, Javier, Liu, Ying, Callesen, Henrik, Filgueiras-Rama, David, Ibáñez, Borja, Sørensen, Charlotte Brandt, Andrés, Vicente
Vydáno v Cell Discov (2019)