Functionally Essential Tubular Proteins Are Lost to Urine-Excreted, Large Extracellular Vesicles during Chronic Renal Insufficiency

af Adam, Ryan J., Paterson, Mark R., Wardecke, Lukus, Hoffmann, Brian R., Kriegel, Alison J.
Udgivet i Kidney360 (2020)

CFTR potentiation as a therapeutic strategy for pulmonary edema: a proof-of-concept study in pigs

af Li, Xiaopeng, Vargas Buonfiglio, Luis G., Adam, Ryan J., Stoltz, David A., Zabner, Joseph, Comellas, Alejandro P.
Udgivet i Crit Care Med (2017)

Sympathoexcitation in response to cardiac and pulmonary afferent stimulation of TRPA1 channels is attenuated in rats with chronic heart failure

af Adam, Ryan J., Xia, Zhiqiu, Pravoverov, Kristina, Hong, Juan, Case, Adam J., Schultz, Harold D., Lisco, Steven J., Zucker, Irving H., Wang, Han-Jun
Udgivet i Am J Physiol Heart Circ Physiol (2019)

Mounier–Kuhn syndrome: a case of tracheal smooth muscle remodeling

af Cook, Daniel P., Adam, Ryan J., Abou Alaiwa, Mahmoud H., Eberlein, Michael, Klesney‐Tait, Julia A., Parekh, Kalpaj R., Meyerholz, David K., Stoltz, David A.
Udgivet i Clin Case Rep (2016)

CF airway smooth muscle transcriptome reveals a role for PYK2

af Cook, Daniel P., Adam, Ryan J., Zarei, Keyan, Deonovic, Benjamin, Stroik, Mallory R., Gansemer, Nicholas D., Meyerholz, David K., Au, Kin Fai, Stoltz, David A.
Udgivet i JCI Insight (2017)

Macrophage activation in stellate ganglia contributes to lung injury-induced arrhythmogenesis in male rats

af Hong, Juan, Adam, Ryan J., Gao, Lie, Hahka, Taija, Xia, Zhiqiu, Wang, Dong, Nicholas, Thomas A., Zucker, Irving H., Lisco, Steven J., Wang, Han-Jun
Udgivet i Acta Physiol (Oxf) (2021)

Tracheomalacia is associated with lower FEV(1) and Pseudomonas acquisition in children with CF

af Fischer, Anthony J., Singh, Sachinkumar B., Adam, Ryan J., Stoltz, David A., Baranano, Christopher F., Kao, Simon, Weinberger, Miles M., McCray, Paul B., Starner, Timothy D.
Udgivet i Pediatr Pulmonol (2013)

Acid-Sensing Ion Channel 1a Contributes to Airway Hyperreactivity in Mice

af Reznikov, Leah R., Meyerholz, David K., Adam, Ryan J., Abou Alaiwa, Mahmoud, Jaffer, Omar, Michalski, Andrew S., Powers, Linda S., Price, Margaret P., Stoltz, David A., Welsh, Michael J.
Udgivet i PLoS One (2016)

Integrin α6β4 Identifies Human Distal Lung Epithelial Progenitor Cells with Potential as a Cell-Based Therapy for Cystic Fibrosis Lung Disease

af Li, Xiaopeng, Rossen, Nathan, Sinn, Patrick L., Hornick, Andrew L., Steines, Benjamin R., Karp, Philip H., Ernst, Sarah E., Adam, Ryan J., Moninger, Thomas O., Levasseur, Dana N., Zabner, Joseph
Udgivet 2013

SONOGRAPHIC EVIDENCE OF ABNORMAL TRACHEAL CARTILAGE RING STRUCTURE IN CYSTIC FIBROSIS

af Diwakar, Amit, Adam, Ryan J., Michalski, Andrew S., Tamegnon, Monelle M., Fischer, Anthony J., Launspach, Jan L., Horan, Rebecca A., Kao, Simon C., Chaloner, Kathryn, Meyerholz, David K., Stoltz, David A.
Udgivet i Laryngoscope (2015)

Early Airway Structural Changes in Cystic Fibrosis Pigs as a Determinant of Particle Distribution and Deposition

af Awadalla, Maged, Miyawaki, Shinjiro, Alaiwa, Mahmoud H. Abou, Adam, Ryan J., Bouzek, Drake C., Michalski, Andrew S., Fuld, Matthew K., Reynolds, Karen J., Hoffman, Eric A., Lin, Ching-Long, Stoltz, David A.
Udgivet 2013

Assessing mucociliary transport of single particles in vivo shows variable speed and preference for the ventral trachea in newborn pigs

af Hoegger, Mark J., Awadalla, Maged, Namati, Eman, Itani, Omar A., Fischer, Anthony J., Tucker, Alexander J., Adam, Ryan J., McLennan, Geoffrey, Hoffman, Eric A., Stoltz, David A., Welsh, Michael J.
Udgivet 2014

Postnatal airway growth in cystic fibrosis piglets

af Adam, Ryan J., Abou Alaiwa, Mahmoud H., Bouzek, Drake C., Cook, Daniel P., Gansemer, Nicholas D., Taft, Peter J., Powers, Linda S., Stroik, Mallory R., Hoegger, Mark J., McMenimen, James D., Hoffman, Eric A., Zabner, Joseph, Welsh, Michael J., Meyerholz, David K., Stoltz, David A.
Udgivet i J Appl Physiol (1985) (2017)

Lack of cystic fibrosis transmembrane conductance regulator disrupts fetal airway development in pigs

af Meyerholz, David K., Stoltz, David A., Gansemer, Nick D., Ernst, Sarah E., Cook, Daniel P., Strub, Matthew D., LeClair, Erica N., Barker, Carrie K., Adam, Ryan J., Leidinger, Mariah R., Gibson-Corley, Katherine N., Karp, Philip H., Welsh, Michael J., McCray, Paul B.
Udgivet i Lab Invest (2018)

Air Trapping and Airflow Obstruction in Newborn Cystic Fibrosis Piglets

af Adam, Ryan J., Michalski, Andrew S., Bauer, Christian, Abou Alaiwa, Mahmoud H., Gross, Thomas J., Awadalla, Maged S., Bouzek, Drake C., Gansemer, Nicholas D., Taft, Peter J., Hoegger, Mark J., Diwakar, Amit, Ochs, Matthias, Reinhardt, Joseph M., Hoffman, Eric A., Beichel, Reinhard R., Meyerholz, David K., Stoltz, David A.
Udgivet 2013

Acute administration of ivacaftor to people with cystic fibrosis and a G551D-CFTR mutation reveals smooth muscle abnormalities

af Adam, Ryan J., Hisert, Katherine B., Dodd, Jonathan D., Grogan, Brenda, Launspach, Janice L., Barnes, Janel K., Gallagher, Charles G., Sieren, Jered P., Gross, Thomas J., Fischer, Anthony J., Cavanaugh, Joseph E., Hoffman, Eric A., Singh, Pradeep K., Welsh, Michael J., McKone, Edward F., Stoltz, David A.
Udgivet i JCI Insight (2016)

Restoring Cystic Fibrosis Transmembrane Conductance Regulator Function Reduces Airway Bacteria and Inflammation in People with Cystic Fibrosis and Chronic Lung Infections

af Hisert, Katherine B., Heltshe, Sonya L., Pope, Christopher, Jorth, Peter, Wu, Xia, Edwards, Rachael M., Radey, Matthew, Accurso, Frank J., Wolter, Daniel J., Cooke, Gordon, Adam, Ryan J., Carter, Suzanne, Grogan, Brenda, Launspach, Janice L., Donnelly, Seamas C., Gallagher, Charles G., Bruce, James E., Stoltz, David A., Welsh, Michael J., Hoffman, Lucas R., McKone, Edward F., Singh, Pradeep K.
Udgivet i Am J Respir Crit Care Med (2017)

Intestinal CFTR expression alleviates meconium ileus in cystic fibrosis pigs

af Stoltz, David A., Rokhlina, Tatiana, Ernst, Sarah E., Pezzulo, Alejandro A., Ostedgaard, Lynda S., Karp, Philip H., Samuel, Melissa S., Reznikov, Leah R., Rector, Michael V., Gansemer, Nicholas D., Bouzek, Drake C., Alaiwa, Mahmoud H. Abou, Hoegger, Mark J., Ludwig, Paula S., Taft, Peter J., Wallen, Tanner J., Wohlford-Lenane, Christine, McMenimen, James D., Chen, Jeng-Haur, Bogan, Katrina L., Adam, Ryan J., Hornick, Emma E., Nelson, George A., Hoffman, Eric A., Chang, Eugene H., Zabner, Joseph, McCray, Paul B., Prather, Randall S., Meyerholz, David K., Welsh, Michael J.
Udgivet 2013