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Restoring Cystic Fibrosis Transmembrane Conductance Regulator Function Reduces Airway Bacteria and Inflammation in People with Cystic Fibrosis and Chronic Lung Infections

Rationale: Previous work indicates that ivacaftor improves cystic fibrosis transmembrane conductance regulator (CFTR) activity and lung function in people with cystic fibrosis and G551D-CFTR mutations but does not reduce density of bacteria or markers of inflammation in the airway. These findings ra...

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Pubblicato in:Am J Respir Crit Care Med
Autori principali: Hisert, Katherine B., Heltshe, Sonya L., Pope, Christopher, Jorth, Peter, Wu, Xia, Edwards, Rachael M., Radey, Matthew, Accurso, Frank J., Wolter, Daniel J., Cooke, Gordon, Adam, Ryan J., Carter, Suzanne, Grogan, Brenda, Launspach, Janice L., Donnelly, Seamas C., Gallagher, Charles G., Bruce, James E., Stoltz, David A., Welsh, Michael J., Hoffman, Lucas R., McKone, Edward F., Singh, Pradeep K.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Thoracic Society 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5476912/
https://ncbi.nlm.nih.gov/pubmed/28222269
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1164/rccm.201609-1954OC
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