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Distinct Functional Domains of Nibrin Mediate Mre11 Binding, Focus Formation, and Nuclear Localization

The inherited chromosomal instability disorder Nijmegen breakage syndrome (NBS) results from truncating mutations in the NBS1 gene, which encodes the protein nibrin. Nibrin is part of a nuclear multiprotein complex that also contains the DNA repair proteins Mre11 and Rad50. Upon irradiation, this co...

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Autors principals: Desai-Mehta, Ami, Cerosaletti, Karen M., Concannon, Patrick
Format: Artigo
Idioma:Inglês
Publicat: American Society for Microbiology 2001
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC86852/
https://ncbi.nlm.nih.gov/pubmed/11238951
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1128/MCB.21.6.2184-2191.2001
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