Thymic Epithelial Cell Alterations and Defective Thymopoiesis Lead to Central and Peripheral Tolerance Perturbation in MHCII Deficiency

Major Histocompatibility Complex (MHC) class II (MHCII) deficiency (MHCII-D), also known as Bare Lymphocyte Syndrome (BLS), is a rare combined immunodeficiency due to mutations in genes regulating expression of MHCII molecules. MHCII deficiency results in impaired cellular and humoral immune respons...

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書誌詳細
出版年:Front Immunol
主要な著者: Ferrua, Francesca, Bortolomai, Ileana, Fontana, Elena, Di Silvestre, Dario, Rigoni, Rosita, Marcovecchio, Genni Enza, Draghici, Elena, Brambilla, Francesca, Castiello, Maria Carmina, Delfanti, Gloria, Moshous, Despina, Picard, Capucine, Taghon, Tom, Bordon, Victoria, Schulz, Ansgar S., Schuetz, Catharina, Giliani, Silvia, Soresina, Annarosa, Gennery, Andrew R., Signa, Sara, Dávila Saldaña, Blachy J., Delmonte, Ottavia M., Notarangelo, Luigi D., Roifman, Chaim M., Poliani, Pietro Luigi, Uva, Paolo, Mauri, Pier Luigi, Villa, Anna, Bosticardo, Marita
フォーマット: Artigo
言語:Inglês
出版事項: Frontiers Media S.A. 2021
主題:
Immunology
オンライン･アクセス:https://ncbi.nlm.nih.gov/pmc/articles/PMC8239840/
https://ncbi.nlm.nih.gov/pubmed/34211466
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2021.669943
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