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Actin Remodeling Defects Leading to Autoinflammation and Immune Dysregulation

A growing number of monogenic immune-mediated diseases have been related to genes involved in pathways of actin cytoskeleton remodeling. Increasing evidences associate cytoskeleton defects to autoinflammatory diseases and primary immunodeficiencies. We reviewed the pathways of actin cytoskeleton rem...

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發表在:Front Immunol
Main Authors: Papa, Riccardo, Penco, Federica, Volpi, Stefano, Gattorno, Marco
格式: Artigo
語言:Inglês
出版: Frontiers Media S.A. 2021
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在線閱讀:https://ncbi.nlm.nih.gov/pmc/articles/PMC7817698/
https://ncbi.nlm.nih.gov/pubmed/33488606
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.604206
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