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Actin Remodeling Defects Leading to Autoinflammation and Immune Dysregulation

A growing number of monogenic immune-mediated diseases have been related to genes involved in pathways of actin cytoskeleton remodeling. Increasing evidences associate cytoskeleton defects to autoinflammatory diseases and primary immunodeficiencies. We reviewed the pathways of actin cytoskeleton rem...

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Détails bibliographiques
Publié dans:Front Immunol
Auteurs principaux: Papa, Riccardo, Penco, Federica, Volpi, Stefano, Gattorno, Marco
Format: Artigo
Langue:Inglês
Publié: Frontiers Media S.A. 2021
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC7817698/
https://ncbi.nlm.nih.gov/pubmed/33488606
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.604206
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