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Actin Remodeling Defects Leading to Autoinflammation and Immune Dysregulation

A growing number of monogenic immune-mediated diseases have been related to genes involved in pathways of actin cytoskeleton remodeling. Increasing evidences associate cytoskeleton defects to autoinflammatory diseases and primary immunodeficiencies. We reviewed the pathways of actin cytoskeleton rem...

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Detalhes bibliográficos
Publicado no:Front Immunol
Main Authors: Papa, Riccardo, Penco, Federica, Volpi, Stefano, Gattorno, Marco
Formato: Artigo
Idioma:Inglês
Publicado em: Frontiers Media S.A. 2021
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC7817698/
https://ncbi.nlm.nih.gov/pubmed/33488606
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fimmu.2020.604206
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