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Purifying Selection against Pathogenic Mitochondrial DNA in Human T Cells

Many mitochondrial diseases are caused by mutations in mitochondrial DNA (mtDNA). Patients’ cells contain a mixture of mutant and nonmutant mtDNA (a phenomenon called heteroplasmy). The proportion of mutant mtDNA varies across patients and among tissues within a patient. We simultaneously assayed si...

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Detalles Bibliográficos
Publicado en:N Engl J Med
Main Authors: Walker, Melissa A., Lareau, Caleb A., Ludwig, Leif S., Karaa, Amel, Sankaran, Vijay G., Regev, Aviv, Mootha, Vamsi K.
Formato: Artigo
Idioma:Inglês
Publicado: 2020
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC7593775/
https://ncbi.nlm.nih.gov/pubmed/32786181
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1056/NEJMoa2001265
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