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Pan-enteric neuropathy and dysmotility are present in a mouse model of short-segment Hirschsprung disease and may contribute to post-pullthrough morbidity

PURPOSE: Hirschsprung disease (HSCR) is characterized by distal intestinal aganglionosis. While surgery is lifesaving, gastrointestinal (GI) motility disorders persist in many patients. Our objective was to determine whether enteric nervous system (ENS) abnormalities exist in the ganglionated portio...

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Bibliografski detalji
Izdano u:J Pediatr Surg
Glavni autori: Bhave, Sukhada, Arciero, Emily, Baker, Corey, Ho, Wing Lam, Guyer, Richard A., Hotta, Ryo, Goldstein, Allan M.
Format: Artigo
Jezik:Inglês
Izdano: 2020
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC7572464/
https://ncbi.nlm.nih.gov/pubmed/32414519
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jpedsurg.2020.04.002
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