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Pan-enteric neuropathy and dysmotility are present in a mouse model of short-segment Hirschsprung disease and may contribute to post-pullthrough morbidity

PURPOSE: Hirschsprung disease (HSCR) is characterized by distal intestinal aganglionosis. While surgery is lifesaving, gastrointestinal (GI) motility disorders persist in many patients. Our objective was to determine whether enteric nervous system (ENS) abnormalities exist in the ganglionated portio...

Täydet tiedot

Tallennettuna:
Bibliografiset tiedot
Julkaisussa:J Pediatr Surg
Päätekijät: Bhave, Sukhada, Arciero, Emily, Baker, Corey, Ho, Wing Lam, Guyer, Richard A., Hotta, Ryo, Goldstein, Allan M.
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: 2020
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC7572464/
https://ncbi.nlm.nih.gov/pubmed/32414519
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jpedsurg.2020.04.002
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