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Mitochondrial Proteome of Affected Glutamatergic Neurons in a Mouse Model of Leigh Syndrome

Defects in mitochondrial function lead to severe neuromuscular orphan pathologies known as mitochondrial disease. Among them, Leigh Syndrome is the most common pediatric presentation, characterized by symmetrical brain lesions, hypotonia, motor and respiratory deficits, and premature death. Mitochon...

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Dettagli Bibliografici
Pubblicato in:Front Cell Dev Biol
Autori principali: Gella, Alejandro, Prada-Dacasa, Patricia, Carrascal, Montserrat, Urpi, Andrea, González-Torres, Melania, Abian, Joaquin, Sanz, Elisenda, Quintana, Albert
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2020
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC7399339/
https://ncbi.nlm.nih.gov/pubmed/32850799
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fcell.2020.00660
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