Caricamento...

Loss of Mitochondrial Ndufs4 in Striatal Medium Spiny Neurons Mediates Progressive Motor Impairment in a Mouse Model of Leigh Syndrome

Inability of mitochondria to generate energy leads to severe and often fatal myoencephalopathies. Among these, Leigh syndrome (LS) is one of the most common childhood mitochondrial diseases; it is characterized by hypotonia, failure to thrive, respiratory insufficiency and progressive mental and mot...

Descrizione completa

Salvato in:
Dettagli Bibliografici
Pubblicato in:Front Mol Neurosci
Autori principali: Chen, Byron, Hui, Jessica, Montgomery, Kelsey S., Gella, Alejandro, Bolea, Irene, Sanz, Elisenda, Palmiter, Richard D., Quintana, Albert
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2017
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5573716/
https://ncbi.nlm.nih.gov/pubmed/28883788
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnmol.2017.00265
Tags: Aggiungi Tag
Nessun Tag, puoi essere il primo ad aggiungerne! !