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Hepatic glutamine synthetase augmentation enhances ammonia detoxification.

The urea cycle and glutamine synthetase (GS) are the two main pathways for waste nitrogen removal and their deficiency results in hyperammonemia. Here, we investigated the efficacy of liver-specific GS overexpression for therapy of hyperammonemia. To achieve hepatic GS overexpression, we generated a...

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Dades bibliogràfiques
Publicat a:J Inherit Metab Dis
Autors principals: Soria, Leandro R., Nitzahn, Matthew, Angelis, Angela De, Khoja, Suhail, Attanasio, Sergio, Annunziata, Patrizia, Palmer, Donna J., Ng, Philip, Lipshutz, Gerald S., Brunetti-Pierri, Nicola
Format: Artigo
Idioma:Inglês
Publicat: 2019
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC6684872/
https://ncbi.nlm.nih.gov/pubmed/30724386
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jimd.12070
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