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Defective proteostasis in celiac disease as a new therapeutic target

Cystic fibrosis (CF) is a disease caused by loss-of-function mutations affecting the CF transmembrane conductance regulator (CFTR), a chloride channel. Recent evidence indicates that CFTR is inhibited by a gluten/gliadin-derived peptide (P31-43), causing an acquired state of CFTR inhibition within t...

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Detalhes bibliográficos
Publicado no:Cell Death Dis
Main Authors: Maiuri, Luigi, Villella, Valeria R, Piacentini, Mauro, Raia, Valeria, Kroemer, Guido
Formato: Artigo
Idioma:Inglês
Publicado em: Nature Publishing Group UK 2019
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC6368542/
https://ncbi.nlm.nih.gov/pubmed/30737369
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/s41419-019-1392-9
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