Manipulating proteostasis to repair the F508del-CFTR defect in cystic fibrosis

Gelijkaardige items

• Cystic fibrosis transmembrane conductance regulator (CFTR) and autophagy: hereditary defects in cystic fibrosis versus gluten-mediated inhibition in celiac disease
  door: Maiuri, Luigi, et al.
  Gepubliceerd in: (2019)
• Targeting the Intracellular Environment in Cystic Fibrosis: Restoring Autophagy as a Novel Strategy to Circumvent the CFTR Defect
  door: Villella, Valeria Rachela, et al.
  Gepubliceerd in: (2013)
• The holy grail of cystic fibrosis research: pharmacological repair of the F508del-CFTR mutation
  door: Maiuri, Luigi, et al.
  Gepubliceerd in: (2015)
• Cysteamine re-establishes the clearance of Pseudomonas aeruginosa by macrophages bearing the cystic fibrosis-relevant F508del-CFTR mutation
  door: Ferrari, Eleonora, et al.
  Gepubliceerd in: (2017)
• Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutation
  door: Stefano, Daniela De, et al.
  Gepubliceerd in: (2014)