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Proteostasis in Huntington's disease: disease mechanisms and therapeutic opportunities

Many neurodegenerative diseases are characterized by impairment of protein quality control mechanisms in neuronal cells. Ineffective clearance of misfolded proteins by the proteasome, autophagy pathways and exocytosis leads to accumulation of toxic protein oligomers and aggregates in neurons. Toxic...

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Dades bibliogràfiques
Publicat a:Acta Pharmacol Sin
Autors principals: Harding, Rachel J, Tong, Yu-feng
Format: Artigo
Idioma:Inglês
Publicat: Nature Publishing Group 2018
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5943907/
https://ncbi.nlm.nih.gov/pubmed/29620053
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/aps.2018.11
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