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Mutant Huntingtin Is Secreted via a Late Endosomal/Lysosomal Unconventional Secretory Pathway

Huntington's disease (HD) is an autosomal-dominant neurodegenerative disorder caused by the expansion of a CAG triplet in the gene encoding for huntingtin (Htt). The resulting mutant protein (mHtt) with extended polyglutamine (polyQ) sequence at the N terminus leads to neuronal degeneration bot...

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Pubblicato in:J Neurosci
Autori principali: Trajkovic, Katarina, Jeong, Hyunkyung, Krainc, Dimitri
Natura: Artigo
Lingua:Inglês
Pubblicazione: Society for Neuroscience 2017
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC5597981/
https://ncbi.nlm.nih.gov/pubmed/28821645
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.0118-17.2017
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