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Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences
Cystic fibrosis (CF) is caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR) gene. The resultant characteristic ion transport defect results in decreased mucociliary clearance, bacterial colonisation, and chronic neutrophil-dominated inflammation. Much knowledge surr...
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| Pubblicato in: | Biomed Res Int |
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| Autori principali: | , , , , |
| Natura: | Artigo |
| Lingua: | Inglês |
| Pubblicazione: |
Hindawi Publishing Corporation
2016
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| Soggetti: | |
| Accesso online: | https://ncbi.nlm.nih.gov/pmc/articles/PMC4908263/ https://ncbi.nlm.nih.gov/pubmed/27340661 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2016/5258727 |
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