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Deficiency of the Survival of Motor Neuron Protein Impairs mRNA Localization and Local Translation in the Growth Cone of Motor Neurons

Spinal muscular atrophy (SMA) is a neurodegenerative disease primarily affecting spinal motor neurons. It is caused by reduced levels of the survival of motor neuron (SMN) protein, which plays an essential role in the biogenesis of spliceosomal small nuclear ribonucleoproteins in all tissues. The et...

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Detalles Bibliográficos
Publicado en:J Neurosci
Main Authors: Fallini, Claudia, Donlin-Asp, Paul G., Rouanet, Jeremy P., Bassell, Gary J., Rossoll, Wilfried
Formato: Artigo
Idioma:Inglês
Publicado: Society for Neuroscience 2016
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC4812137/
https://ncbi.nlm.nih.gov/pubmed/27030765
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.2396-15.2016
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