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Sirolimus Decreases Circulating Lymphangioleiomyomatosis Cells in Patients With Lymphangioleiomyomatosis

BACKGROUND: Lymphangioleiomyomatosis (LAM), sporadic or in women with tuberous sclerosis complex (TSC), is characterized by cystic lung destruction, lymphatic involvement (eg, chylous pleural effusions, lymphangioleiomyomas), and renal angiomyolipomas (AMLs). The multisystem manifestations of LAM ap...

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Détails bibliographiques
Auteurs principaux: Cai, Xiong, Pacheco-Rodriguez, Gustavo, Haughey, Mary, Samsel, Leigh, Xu, Suowen, Wu, Hai-Ping, McCoy, J. Philip, Stylianou, Mario, Darling, Thomas N., Moss, Joel
Format: Artigo
Langue:Inglês
Publié: American College of Chest Physicians 2014
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC3883264/
https://ncbi.nlm.nih.gov/pubmed/24051985
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1378/chest.13-1071
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