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Sirolimus Decreases Circulating Lymphangioleiomyomatosis Cells in Patients With Lymphangioleiomyomatosis

BACKGROUND: Lymphangioleiomyomatosis (LAM), sporadic or in women with tuberous sclerosis complex (TSC), is characterized by cystic lung destruction, lymphatic involvement (eg, chylous pleural effusions, lymphangioleiomyomas), and renal angiomyolipomas (AMLs). The multisystem manifestations of LAM ap...

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Bibliografiset tiedot
Päätekijät: Cai, Xiong, Pacheco-Rodriguez, Gustavo, Haughey, Mary, Samsel, Leigh, Xu, Suowen, Wu, Hai-Ping, McCoy, J. Philip, Stylianou, Mario, Darling, Thomas N., Moss, Joel
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: American College of Chest Physicians 2014
Aiheet:
Linkit:https://ncbi.nlm.nih.gov/pmc/articles/PMC3883264/
https://ncbi.nlm.nih.gov/pubmed/24051985
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1378/chest.13-1071
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