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Sirolimus Decreases Circulating Lymphangioleiomyomatosis Cells in Patients With Lymphangioleiomyomatosis

BACKGROUND: Lymphangioleiomyomatosis (LAM), sporadic or in women with tuberous sclerosis complex (TSC), is characterized by cystic lung destruction, lymphatic involvement (eg, chylous pleural effusions, lymphangioleiomyomas), and renal angiomyolipomas (AMLs). The multisystem manifestations of LAM ap...

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Detalhes bibliográficos
Main Authors: Cai, Xiong, Pacheco-Rodriguez, Gustavo, Haughey, Mary, Samsel, Leigh, Xu, Suowen, Wu, Hai-Ping, McCoy, J. Philip, Stylianou, Mario, Darling, Thomas N., Moss, Joel
Formato: Artigo
Idioma:Inglês
Publicado em: American College of Chest Physicians 2014
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3883264/
https://ncbi.nlm.nih.gov/pubmed/24051985
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1378/chest.13-1071
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