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Dopaminergic Signaling and Striatal Neurodegeneration in Huntington's Disease

Huntington's disease (HD) is a neurodegenerative disorder caused by polyglutamine (polyQ) expansion in Huntingtin protein (Htt). PolyQ expansion in Htt(exp) causes selective degeneration of striatal medium spiny neurons (MSNs) in HD patients. Striatal MSN neurons receive glutamatergic input fro...

Disgrifiad llawn

Wedi'i Gadw mewn:
Manylion Llyfryddiaeth
Prif Awduron: Tang, Tie-Shan, Chen, Xi, Liu, Jing, Bezprozvanny, Ilya
Fformat: Artigo
Iaith:Inglês
Cyhoeddwyd: Society for Neuroscience 2007
Pynciau:
Mynediad Ar-lein:https://ncbi.nlm.nih.gov/pmc/articles/PMC3307545/
https://ncbi.nlm.nih.gov/pubmed/17652581
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.1396-07.2007
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