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Dopaminergic Signaling and Striatal Neurodegeneration in Huntington's Disease

Huntington's disease (HD) is a neurodegenerative disorder caused by polyglutamine (polyQ) expansion in Huntingtin protein (Htt). PolyQ expansion in Htt(exp) causes selective degeneration of striatal medium spiny neurons (MSNs) in HD patients. Striatal MSN neurons receive glutamatergic input fro...

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Autors principals: Tang, Tie-Shan, Chen, Xi, Liu, Jing, Bezprozvanny, Ilya
Format: Artigo
Idioma:Inglês
Publicat: Society for Neuroscience 2007
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3307545/
https://ncbi.nlm.nih.gov/pubmed/17652581
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.1396-07.2007
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