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TDP-43 and FUS/TLS: emerging roles in RNA processing and neurodegeneration

Amyotrophic lateral sclerosis (ALS) and frontotemporal lobar degeneration (FTLD) are neurodegenerative diseases with clinical and pathological overlap. Landmark discoveries of mutations in the transactive response DNA-binding protein (TDP-43) and fused in sarcoma/translocated in liposarcoma (FUS/TLS...

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Detalles Bibliográficos
Main Authors: Lagier-Tourenne, Clotilde, Polymenidou, Magdalini, Cleveland, Don W.
Formato: Artigo
Idioma:Inglês
Publicado: Oxford University Press 2010
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3167692/
https://ncbi.nlm.nih.gov/pubmed/20400460
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddq137
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