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Modeling spinal muscular atrophy in Drosophila links Smn to FGF signaling

Spinal muscular atrophy (SMA), a devastating neurodegenerative disorder characterized by motor neuron loss and muscle atrophy, has been linked to mutations in the Survival Motor Neuron (SMN) gene. Based on an SMA model we developed in Drosophila, which displays features that are analogous to the hum...

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Dettagli Bibliografici
Autori principali: Sen, Anindya, Yokokura, Takakazu, Kankel, Mark W., Dimlich, Douglas N., Manent, Jan, Sanyal, Subhabrata, Artavanis-Tsakonas, Spyros
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Rockefeller University Press 2011
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3101100/
https://ncbi.nlm.nih.gov/pubmed/21300852
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.201004016
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