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Huntington disease models and human neuropathology: similarities and differences
Huntington disease (HD) occurs only in humans. Thus, its natural pathogenesis takes place exclusively within the human brains expressing the causative, mutated protein huntingtin (mhtt). The techniques applicable to postmortem human HD brains are inadequate for investigating the cellular pathogenesi...
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| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
2007
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| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC2847401/ https://ncbi.nlm.nih.gov/pubmed/17978822 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00401-007-0306-6 |
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