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Huntington disease models and human neuropathology: similarities and differences

Huntington disease (HD) occurs only in humans. Thus, its natural pathogenesis takes place exclusively within the human brains expressing the causative, mutated protein huntingtin (mhtt). The techniques applicable to postmortem human HD brains are inadequate for investigating the cellular pathogenesi...

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Autor principal: Vonsattel, Jean Paul G.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2007
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2847401/
https://ncbi.nlm.nih.gov/pubmed/17978822
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00401-007-0306-6
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