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Immunopurification of Pathological Prion Protein Aggregates

BACKGROUND: Prion diseases are fatal neurodegenerative disorders that can arise sporadically, be genetically inherited or acquired through infection. The key event in these diseases is misfolding of the cellular prion protein (PrP(C)) into a pathogenic isoform that is rich in β-sheet structure. This...

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Autori principali: Biasini, Emiliano, Tapella, Laura, Mantovani, Susanna, Stravalaci, Matteo, Gobbi, Marco, Harris, David A., Chiesa, Roberto
Natura: Artigo
Lingua:Inglês
Pubblicazione: Public Library of Science 2009
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2773113/
https://ncbi.nlm.nih.gov/pubmed/19915706
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0007816
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