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Reduced Translocation of Nascent Prion Protein During ER Stress Contributes to Neurodegeneration

During acute stress in the endoplasmic reticulum (ER), mammalian prion protein (PrP) is temporarily prevented from translocation into the ER and instead routed directly for cytosolic degradation. This ‘pre-emptive’ quality control (pQC) system benefits cells by minimizing PrP aggregation in the secr...

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Bibliografske podrobnosti
Main Authors: Rane, Neena S., Kang, Sang-Wook, Chakrabarti, Oishee, Feigenbaum, Lionel, Hegde, Ramanujan S.
Format: Artigo
Jezik:Inglês
Izdano: 2008
Teme:
Online dostop:https://ncbi.nlm.nih.gov/pmc/articles/PMC2563805/
https://ncbi.nlm.nih.gov/pubmed/18804434
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.devcel.2008.06.015
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