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Reduced Threshold for Luminal Ca(2+) Activation of RyR1 Underlies a Causal Mechanism of Porcine Malignant Hyperthermia

Naturally occurring mutations in the skeletal muscle Ca(2+) release channel/ryanodine receptor RyR1 are linked to malignant hyperthermia (MH), a life-threatening complication of general anesthesia. Although it has long been recognized that MH results from uncontrolled or spontaneous Ca(2+) release f...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Jiang, Dawei, Chen, Wenqian, Xiao, Jianmin, Wang, Ruiwu, Kong, Huihui, Jones, Peter P., Zhang, Lin, Fruen, Bradley, Chen, S. R. Wayne
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: American Society for Biochemistry and Molecular Biology 2008
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC2475718/
https://ncbi.nlm.nih.gov/pubmed/18505726
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M801944200
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