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M line–deficient titin causes cardiac lethality through impaired maturation of the sarcomere

Titin, the largest protein known to date, has been linked to sarcomere assembly and function through its elastic adaptor and signaling domains. Titin's M-line region contains a unique kinase domain that has been proposed to regulate sarcomere assembly via its substrate titin cap (T-cap). In thi...

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Autors principals: Weinert, Stefanie, Bergmann, Nora, Luo, Xiuju, Erdmann, Bettina, Gotthardt, Michael
Format: Artigo
Idioma:Inglês
Publicat: The Rockefeller University Press 2006
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2063865/
https://ncbi.nlm.nih.gov/pubmed/16702235
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.200601014
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