Targets for cystic fibrosis therapy: proteomic analysis and correction of mutant cystic fibrosis transmembrane conductance regulator

بواسطة Collawn, James F, Fu, Lianwu, Bebok, Zsuzsa
منشور في 2010

The CFTR and ENaC debate: how important is ENaC in CF lung disease?

بواسطة Collawn, James F., Lazrak, Ahmed, Bebok, Zsuzsa, Matalon, Sadis
منشور في 2012

Characterization and Dynamics of Aggresome Formation by a Cytosolic Gfp-Chimera✪

بواسطة García-Mata, Rafael, Bebök, Zsuzsa, Sorscher, Eric J., Sztul, Elizabeth S.
منشور في 1999

CFTR Expression Regulation by the Unfolded Protein Response

بواسطة Bartoszewski, Rafal, Rab, Andras, Fu, Lianwu, Bartoszewska, Sylwia, Collawn, James, Bebok, Zsuzsa
الحاوية / القاعدة Methods Enzymol (2011)

Regulation of angiogenesis by hypoxia: the role of microRNA

بواسطة Madanecki, Piotr, Kapoor, Niren, Bebok, Zsuzsa, Ochocka, Renata, Collawn, James F., Bartoszewski, Rafal
منشور في 2012

Cigarette smoke and CFTR: implications in the pathogenesis of COPD

بواسطة Rab, Andras, Rowe, Steven M., Raju, S. Vamsee, Bebok, Zsuzsa, Matalon, Sadis, Collawn, James F.
منشور في 2013

Activation of the Unfolded Protein Response by ΔF508 CFTR

بواسطة Bartoszewski, Rafal, Rab, Andras, Jurkuvenaite, Asta, Mazur, Marina, Wakefield, John, Collawn, James F., Bebők, Zsuzsa
منشور في 2008

Functional Stability of Rescued ΔF508 Cystic Fibrosis Transmembrane Conductance Regulator in Airway Epithelial Cells

بواسطة Jurkuvenaite, Asta, Chen, Lan, Bartoszewski, Rafal, Goldstein, Rebecca, Bebok, Zsuzsa, Matalon, Sadis, Collawn, James F.
منشور في 2010

Dab2 is a Key Regulator of Endocytosis and Post-endocytic Trafficking of the Cystic Fibrosis Transmembrane Conductance Regulator

بواسطة Fu, Lianwu, Rab, Andras, Tang, Li Ping, Rowe, Steven M., Bebok, Zsuzsa, Collawn, James F.
منشور في 2012

ΔF508 CFTR Surface Stability Is Regulated by DAB2 and CHIP-Mediated Ubiquitination in Post-Endocytic Compartments

بواسطة Fu, Lianwu, Rab, Andras, Tang, Li ping, Bebok, Zsuzsa, Rowe, Steven M., Bartoszewski, Rafal, Collawn, James F.
الحاوية / القاعدة PLoS One (2015)

miR-200b downregulates CFTR during hypoxia in human lung epithelial cells

بواسطة Bartoszewska, Sylwia, Kamysz, Wojciech, Jakiela, Bogdan, Sanak, Marek, Króliczewski, Jarosław, Bebok, Zsuzsa, Bartoszewski, Rafal, Collawn, James F.
الحاوية / القاعدة Cell Mol Biol Lett (2017)

Failure of cAMP agonists to activate rescued ΔF508 CFTR in CFBE41o(–) airway epithelial monolayers

بواسطة Bebok, Zsuzsa, Collawn, James F, Wakefield, John, Parker, William, Li, Yao, Varga, Karoly, Sorscher, Eric J, Clancy, JP
منشور في 2005

A Synonymous Single Nucleotide Polymorphism in ΔF508 CFTR Alters the Secondary Structure of the mRNA and the Expression of the Mutant Protein

بواسطة Bartoszewski, Rafal A., Jablonsky, Michael, Bartoszewska, Sylwia, Stevenson, Lauren, Dai, Qun, Kappes, John, Collawn, James F., Bebok, Zsuzsa
منشور في 2010

VCP/p97 AAA-ATPase Does Not Interact with the Endogenous Wild-Type Cystic Fibrosis Transmembrane Conductance Regulator

بواسطة Goldstein, Rebecca F., Niraj, Ashutosh, Sanderson, Todd P., Wilson, Landon S., Rab, Andras, Kim, Helen, Bebok, Zsuzsa, Collawn, James F.
منشور في 2007

Restoration of W1282X CFTR Activity by Enhanced Expression

بواسطة Rowe, Steven M., Varga, Karoly, Rab, Andras, Bebok, Zsuzsa, Byram, Kevin, Li, Yao, Sorscher, Eric J., Clancy, John P.
منشور في 2007

BIOELECTRIC EFFECTS OF QUININE ON POLARIZED AIRWAY EPITHELIAL CELLS

بواسطة Rowe, Steven M., Bates, Eleanor, Miller, Stacey, Alexander, Mariah, Mazur, Marina, Fortenberry, James A., Bebok, Zsuzsa, Sorscher, Eric J.
منشور في 2007

The Unfolded Protein Response (UPR)-activated Transcription Factor X-box-binding Protein 1 (XBP1) Induces MicroRNA-346 Expression That Targets the Human Antigen Peptide Transporter...

بواسطة Bartoszewski, Rafal, Brewer, Joseph W., Rab, Andras, Crossman, David K., Bartoszewska, Sylwia, Kapoor, Niren, Fuller, Cathy, Collawn, James F., Bebok, Zsuzsa
منشور في 2011

Suppression of CFTR premature termination codons and rescue of CFTR protein and function by the synthetic aminoglycoside NB54

بواسطة Rowe, Steven M., Sloane, Peter, Tang, Li Ping, Backer, Kyle, Mazur, Marina, Buckley-Lanier, Jessica, Nudelman, Igor, Belakhov, Valery, Bebok, Zsuzsa, Schwiebert, Erik, Baasov, Timor, Bedwell, David M.
منشور في 2011

No Detectable Improvements in Cystic Fibrosis Transmembrane Conductance Regulator by Nasal Aminoglycosides in Patients with Cystic Fibrosis with Stop Mutations

بواسطة Clancy, John P., Rowe, Steven M., Bebok, Zsuzsa, Aitken, Moira L., Gibson, Ron, Zeitlin, Pam, Berclaz, Pierre, Moss, Rick, Knowles, Michael R., Oster, Robert A., Mayer-Hamblett, Nicole, Ramsey, Bonnie
منشور في 2007