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Calcineurin Activity Is Increased in Charcot-Marie-Tooth 1B Demyelinating Neuropathy

Schwann cells produce a considerable amount of lipids and proteins to form myelin in the PNS. For this reason, the quality control of myelin proteins is crucial to ensure proper myelin synthesis. Deletion of serine 63 from P0 (P0S63del) protein in myelin forming Schwann cells causes Charcot-Marie-To...

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Pubblicato in:J Neurosci
Autori principali: Sidoli, Mariapaola, Reed, Chelsey B., Scapin, Cristina, Paez, Pablo, Cavener, Douglas R., Kaufman, Randal J., D'Antonio, Maurizio, Feltri, M. Laura, Wrabetz, Lawrence
Natura: Artigo
Lingua:Inglês
Pubblicazione: Society for Neuroscience 2021
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC8152608/
https://ncbi.nlm.nih.gov/pubmed/33879538
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.2384-20.2021
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