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Ablation of Perk in Schwann Cells Improves Myelination in the S63del Charcot-Marie-Tooth 1B Mouse

In factory cells, the accumulation of misfolded protein provokes the unfolded protein response (UPR). For example, deletion of serine 63 (S63del) in myelin protein zero (P0) induces P0 accumulation in the endoplasmic reticulum (ER) of Schwann cells and a persistent UPR associated with Charcot-Marie-...

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Publicat a:J Neurosci
Autors principals: Sidoli, Mariapaola, Musner, Nicolò, Silvestri, Nicholas, Ungaro, Daniela, D'Antonio, Maurizio, Cavener, Douglas R., Feltri, M. Laura, Wrabetz, Lawrence
Format: Artigo
Idioma:Inglês
Publicat: Society for Neuroscience 2016
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC5148247/
https://ncbi.nlm.nih.gov/pubmed/27807175
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1523/JNEUROSCI.1637-16.2016
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